Respiratory management of spinal muscular atrophy type 2

Research output: Contribution to journalReview article

Abstract

Respiratory insufficiency is the primary cause of morbidity and mortality among patients with spinal muscular atrophy type 2. The primary complications include ineffective cough with decreased airway clearance, nocturnal hypoventilation, diminished lung and chest wall development, and increased risk for pulmonary infection. Respiratory devices including mechanical insufflator-exsufflator and bilevel positive airway pressure are the primary devices of respiratory maintenance and treatment and are associated with decreased morbidity and fewer hospital admissions. This article discusses the primary respiratory complications of spinal muscular atrophy type 2 and the role of respiratory interventions to promote growth and development, improve cough efficacy, reverse nocturnal hypoventilation, and prevent and treat pulmonary infection.

Original languageEnglish (US)
Pages (from-to)E33-E41
JournalJournal of Neuroscience Nursing
Volume46
Issue number6
DOIs
StatePublished - Dec 1 2014

Keywords

  • Bilevel positive airway pressure
  • Ineffective cough
  • Lung and chest wall development
  • Mechanical insufflator-exsufflator
  • Nocturnal hypoventilation
  • Pulmonary infection
  • Respiratory insufficiency
  • Spinal muscular atrophy type 2

ASJC Scopus subject areas

  • Surgery
  • Endocrine and Autonomic Systems
  • Clinical Neurology
  • Medical–Surgical

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